A Review of Behavioral Treatments Used for Lesch-Nyhan Syndrome
Lesch-Nyhan syndrome is a genetic disorder resulting in hyperuricemia, choreoathetosis, mental retardation, and self-mutilation. The most salient feature of this disorder is the self-injurious behavior (SIB). Although the utility of behavioral interventions with SIB has been well documented, behavioral interventions with Lesch-Nyhan syndrome have been limited in number and long-term success. This article reviews the behavioral treatments that have been used in treating individuals with Lesch-Nyhan syndrome and discusses the strengths and weaknesses of these methods. Suggestions for future directions in the use of behavioral interventions for controlling SIB in Lesch-Nyhan syndrome are provided.
Olson, L., & Houlihan, D. (2000). A Review of Behavioral Treatments Used for Lesch-Nyhan Syndrome. Behavior Modification, 24(2), 202-222.
Publisher's Copyright and Source
Copyright © SAGE Publications. Article published by SAGE Publications in Behavior Modification, volume 24, issue number 2, April 2000, pages 202-222. Available online on April 1, 2000: http://doi.org/10.1177/0145445500242003.